GAA Antibody / Glucosidase alpha acid

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.

P10253

Rabbit

A portion of amino acids 174-203 from the human protein were used as the immunogen for the GAA antibody.

Polyclonal

Ig

WB, IHC-P

Purified

In 1X PBS, pH 7.4, with 0.09% sodium azide

Aliquot the GAA antibody and store frozen at -20oC or colder. Avoid repeated freeze-thaw cycles.

This GAA antibody is available for research use only.

Primary antibody

https://www.nsjbio.com/tds/gaa-antibody-f54279